Репозиторий Университета

Год публикации: Все года 2018 2019 2020

Название	Дата публикации	Коллектив авторов	Журнал	DOI	Индекс цитирования	Ссылка на источник
Pregnancy and mesenchimal dysplasias (Marfan syndrome, Ehlers-Danlos syndrome, hereditary hemorrhagic telangiectasia) Ehlers–Danlossyndrome hereditaryhemorrhagictelangiectasia Marfansyndrome Mesenchymaldysplasias pregnancy	03.07.2018	Radetskaya L. Makatsariya A. Bitsadze V. Khizroeva J.	Journal of Maternal-Fetal and Neonatal Medicine		0	Ссылка © 2017 Informa UK Limited, trading as Taylor & Francis Group. The objective of this article is to attract the attention of clinical physicians to the rare but extremely relevant clinical pathology of mesenchymal dysplasias (Marfan syndrome, Ehlers–Danlos syndrome, hereditary hemorrhagic telangiectasia) and especially specific characteristics of such diseases during pregnancy. Connective tissue pathology can cover different organs and systems, symptoms of the same disease can vary in different patients thus making diagnostics significantly difficult. Here clinical diagnostic criteria and methods of molecular diagnostics of diseases are described. The pathogenesis of mesenchymal dysplasias is not currently well understood. For the patients with mesenchymal dysplasias pregnancy is fraught with high risk of life-threatening complications. The preferred delivery method for such patients is caesarean section. Читать тезис
The present-day view on the pathogenesis and prevention of life-threatening complications of pregnancy and delivery in patients with mesenchymal dysplasias (marfan syndrome, ehlers-danlos syndrome, rendu-weber-osler syndrome) Aorticdissectioninpregnantwomen Bleeding Cesareansection Congenitalconnectivetissuediseases Ehlers-danlossyndrome.rendu-weber-osler Marfansyndrome Mesenchymaldysplasias Pregnancy	01.01.2018	Makatsaria A. Radetskaya L.	Akusherstvo i Ginekologiya (Russian Federation)		0	Ссылка © Bionika Media Ltd. Objective. To systematize the current medical knowledge and experience in the management of pregnancy and delivery in patients with mesenchymal dysplasias (Marfan syndrome, Ehlers-Danlos syndrome, Rendu-Osler syndrome). Material and methods. The paper includes the data of foreign investigations and medical guidelines for this problem, which have been published in the past 5 years. Results. The paper describes the molecular bases of each syndrome, diagnostic criteria, and their clinical manifestations in various organs and systems: musculoskeletal and cardiovascular systems, the organ of vision, etc. Such patients during pregnancy are at extremely high risk for life-threatening complications. Conclusion. A successful outcome of pregnancy requires early diagnosis and a multidisciplinary approach throughout during pregnancy and delivery. Читать тезис

Репозиторий Университета

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